What is Insulinomatosis or noninsulinoma pancreatogenous hypoglycaemia (NIPHS)?
Insulinomatosis or NIPHS
An insulinoma is a rare type of functional neuroendocrine tumour which produces insulin and causes hypoglycaemia. A small number of people who complete the diagnosis process for an insulinoma are diagnosed with related conditions:
Insulinomatosis: multiple insulinomas including micro-insulinomas
Proinsulinoma: neuroendocrine tumour which produces proinsulin
Noninsulinoma pancreatogenous hypoglycaemia syndrome (NIPHS): beta cells in the pancreas produce excess insulin without forming a tumour
Useful information:
2023 NIPHS literature review
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